Lactate Dehydrogenase C Produces S-2-Hydroxyglutarate in Mouse Testis. Author Xin Teng, Matthew Emmett, Mitchell Lazar, Erwin Goldberg, Joshua Rabinowitz Publication Year 2016 Type Journal Article Abstract Metabolomics is a valuable tool for studying tissue- and organism-specific metabolism. In normal mouse testis, we found 70 μM S-2-hydroxyglutarate (2HG), more than 10-fold greater than in other tissues. S-2HG is a competitive inhibitor of α-ketoglutarate-dependent demethylation enzymes and can alter histone or DNA methylation. To identify the source of testis S-2HG, we fractionated testis extracts and identified the fractions that actively produced S-2HG. Through a combination of ion exchange and size exclusion chromatography, we enriched a single active protein, the lactate dehydrogenase isozyme LDHC, which is primarily expressed in testis. At neutral pH, recombinant mouse LDHC rapidly converted both pyruvate into lactate and α-ketoglutarate into S-2HG, whereas recombinant human LDHC only produced lactate. Rapid S-2HG production by LDHC depends on amino acids 100-102 being Met-Val-Ser, a sequence that occurs only in the rodent protein. Other mammalian LDH can also produce some S-2HG, but at acidic pH. Thus, polymorphisms in the Ldhc gene control testis levels of S-2HG, and thereby epigenetics, across mammals. Keywords Animals, Mice, Humans, Substrate Specificity, Mice, Inbred C57BL, Male, Mice, Knockout, Isoenzymes, Metabolomics, Testis, DNA Methylation, Glutarates, L-Lactate Dehydrogenase Journal ACS Chem Biol Volume 11 Issue 9 Pages 2420-7 Date Published 2016 Sep 16 ISSN Number 1554-8937 DOI 10.1021/acschembio.6b00290 Alternate Journal ACS Chem Biol PMCID PMC5317044 PMID 27333189 PubMedPubMed CentralGoogle ScholarBibTeXEndNote X3 XML